Molecular and Cellular Pediatrics

Table 1 CF patient demographics

From: miRNA-221 is elevated in cystic fibrosis airway epithelial cells and regulates expression of ATF6

CF	Sex	Age	CFTR genotype	FEV ₁	BMI	PI	Ps .	Sa .	Asp.
1	M	21	ΔF508/R506T > K	17%	30.5	Y	+	+	−
2	M	29	ΔF508/ΔF508	64%	20.24	Y	+	−	−
3	F	25	ΔF508/R177H 5T	89%	23.15	N	-	+	=
4	M	18	ΔF508/ΔF508	87%	20.89	Y	+	+	+
5	M	23	ΔF508/unknown	27%	17.76	Y	+	-	-
6	F	19	ΔF508/ΔF508	54%	21.71	Y	+	-	-
7	F	25	ΔF508/1717GA	51%	19.62	Y	+	-	+
8	M	31	ΔF508/621 + 1G → T	83%	22.77	Y	+	-	+

FEV₁, forced expiratory volume in 1 s percent predicted; BMI, body mass index; PI, pancreatic insufficiency (Y, yes; N, no); Ps., colonisation with Pseudomonas aeruginosa; Sa., colonisation with Staphylococcus aureus; Asp., colonisation with Aspergillus species.

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